Ilgin Yildirim Simsir, Beyhan Tuysuz, Mehmet Nuri Ozbek, Seher Tanrikulu, Merve Celik Guler, Asuman Nur Karhan, Yasemin Denkboy Ongen, Nilay Gunes, Utku Erdem Soyaltin, Canan Altay, Banu Nur, Servan Ozalkak, Ozlem Akgun Dogan, Fatma Dursun, Zafer Pekkolay, Mehmet Ali Eren, Yusuf Usta, Secil Ozisik, Basak Ozgen Saydam, Suleyman Cem Adiyaman, Mehmet Cagri Unal, Gokcen Gungor Semiz, Ihsan Turan, Erdal Eren, Hulya Kayserili, Isabelle Jeru, Corinne Vigouroux, Tahir Atik, Huseyin Onay, Samim Ozen, Elif A Oral, Baris Akinci
AIMS: Without access to leptin replacement, patients with generalized lipodystrophy (GL) are at high risk for severe metabolic disease. Although there is a well-established GL registry in Turkey since the early 2000s, leptin replacement treatment was not available until recently. This gave us a unique opportunity to describe the natural history of GL. METHODS: This study reports on 72 patients with GL (47 families) who were registered at different centers in Turkey that cover all regions of the country...
March 22, 2023: Diabetes, Obesity & Metabolism