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JOURNAL ARTICLE
Ricardo A Arbizu, Sean Trauernicht, Sergio Pinillos, Samuel Nurko, Leonel Rodriguez
OBJECTIVES: Antroduodenal manometry (ADM) measures antral and small bowel motility and is clinically used to evaluate upper gastrointestinal (UGI) symptoms. We aimed to evaluate its utility in guiding treatment, predicting response, and association with clinical findings. METHODS: Retrospective review of 200 children undergoing ADM. ADM interpretation and parameters were compared to outcomes (response to first therapy after ADM and overall response), predominant symptom (group A, abdominal distention and/or vomiting and group B, abdominal pain and/or nausea), etiology (idiopathic or with known comorbidity), and ADM indication (suspected chronic intestinal pseudo-obstruction -CIPO- or unexplained UGI symptoms)...
September 27, 2023: Journal of Pediatric Gastroenterology and Nutrition
#2
REVIEW
Federica Viti, Roberto De Giorgio, Isabella Ceccherini, Arti Ahluwalia, Maria M Alves, Chiara Baldo, Giannina Baldussi, Elena Bonora, Osvaldo Borrelli, Luigi Dall'Oglio, Paolo De Coppi, Carlotta De Filippo, Pascal de Santa Barbara, Antonella Diamanti, Carlo Di Lorenzo, Ruggero Di Maulo, Antonio Galeone, Paolo Gandullia, Sohaib K Hashmi, Florence Lacaille, Laurence Lancon, Salvatore Leone, Maxime M Mahé, Maria Judit Molnar, Alessandro Palmitelli, Silvia Perin, Alessio Pini Prato, Nikhil Thapar, Massimo Vassalli, Robert O Heuckeroth
Visceral myopathy is a rare, life-threatening disease linked to identified genetic mutations in 60% of cases. Mostly due to the dearth of knowledge regarding its pathogenesis, effective treatments are lacking. The disease is most commonly diagnosed in children with recurrent or persistent disabling episodes of functional intestinal obstruction, which can be life threatening, often requiring long-term parenteral or specialized enteral nutritional support. Although these interventions are undisputedly life-saving as they allow affected individuals to avoid malnutrition and related complications, they also seriously compromise their quality of life and can carry the risk of sepsis and thrombosis...
August 31, 2023: Digestive Diseases and Sciences
#3
JOURNAL ARTICLE
Garance Martin, Louise Montalva, Stéphane Paré, Liza Ali, Christine Martinez-Vinson, Anne-Emmanuelle Colas, Arnaud Bonnard
The aim of this study was to compare outcomes of laparoscopic and robotic-assisted colectomy in children. All children who underwent a colectomy with a laparoscopic (LapC) or robotic-assisted (RobC) approach in our institution (January 2010-March 2023) were included. Demographics, surgical data, and post-operative outcomes within 30 days were collected. Additional cost related to the robotic approach was calculated. Comparisons were performed using Fisher tests for categorical variables and Mann-Whitney tests for continuous variables...
June 19, 2023: Journal of Robotic Surgery
#4
JOURNAL ARTICLE
Kitzia Colliard, Samuel Nurko, Alejandro Flores, Leonel Rodriguez
BACKGROUND: Little is known about ileal motility patterns and their utility in children. Here, we present our experience with children undergoing ileal manometry (IM). METHODS: A retrospective review of children with ileostomy comparing IM between two groups: A (chronic intestinal pseudo-obstruction [CIPO]) and B (feasibility of ileostomy closure in children with defecation disorders). We also compared the IM findings with those from antroduodenal manometry (ADM), and evaluated the joint effect of age, sex, and study indication group on IM results...
May 24, 2023: Journal of Pediatric Gastroenterology and Nutrition
#5
JOURNAL ARTICLE
(no author information available yet)
Cystic fibrosis (CF) is one of the most common autosomal recessive genetic diseases in Caucasians, but CF patients in China are rare, and it was listed as the first batch of rare diseases in China in 2018. In recent years, CF has been gradually recognized in China, and the number of CF patients reported in China in the past 10 years is more than 2.5 times the total number in the previous 30 years, and the total number of CF patients is estimated to be more than 20 000. The research progress of CF gene modification has led to the innovation of CF treatment...
April 12, 2023: Chinese Journal of Tuberculosis and Respiratory Diseases
#6
JOURNAL ARTICLE
Giovanni Di Nardo, Letizia Zenzeri, Matteo Guarino, Alessio Molfino, Pasquale Parisi, Giovanni Barbara, Vincenzo Stanghellini, Roberto De Giorgio
INTRODUCTION: Chronic intestinal pseudoobstruction (CIPO) is a rare, heterogenous, and severe form of gastrointestinal dysmotility. AREAS COVERED: Pertinent literature on pediatric and adult CIPO management has been assessed via PubMed, Scopus, and EMBASE from inception to June 2022. Prokinetics, aimed at restoring intestinal propulsion (e.g. orthopramides and substituted benzamides, acetyl cholinesterase inhibitors, serotonergic agents, and others), have been poorly tested and the available data showed only partial efficacy...
April 2023: Expert Review of Gastroenterology & Hepatology
#7
REVIEW
Susan Nham, Alexander T M Nguyen, Andrew J A Holland
Paediatric intestinal pseudo-obstruction (PIPO) encompasses a group of rare disorders in which patients present with the clinical features of bowel obstruction in the absence of mechanical occlusion. The management of PIPO presents a challenge as evidence remains limited on available medical and surgical therapy. Parenteral nutrition is often the mainstay of therapy. Long-term therapy may culminate in life-threatening complications including intestinal failure-related liver disease, central line thrombosis and sepsis...
July 2022: European Journal of Pediatrics
#8
JOURNAL ARTICLE
Francesca Destro, Luciano Maestri, Milena Meroni, Alessandro Campari, Federica Pederiva, Sara Costanzo, Giulia Del Re, Margherita Roveri, Gianvincenzo Zuccotti, Valeria Calcaterra, Gloria Pelizzo
Colonic volvulus (CV) is a rare but potentially life-threatening condition with unclear etiopathogenesis. To date, less than 80 pediatric cases have been described. Hirschsprung's disease (HD) is associated with CV in 17% of cases, representing a significant risk factor. Non-HD CV is an even more complex entity. The aim of this study is to describe a series of patients with CV to accentuate some peculiar aspects of this disease. We performed a retrospective study (period: 2012-2021) collecting information of patients with CV...
October 30, 2021: Children
#9
JOURNAL ARTICLE
Carmina Wanden-Berghe, Nuria Virgili Casas, Cristina Cuerda Compés, Esther Ramos Boluda, José Luis Pereira Cunill, María Irene Maíz Jiménez, Rosa Burgos Peláez, Carmen Gómez Candela, María Ángeles Penacho Lázaro, Eva Ángeles Sánchez Martos, Daniel Antonio de Luis, Ana Zugasti Murillo, Ceferino Martínez Faedo, Julia Álvarez Hernández, Cristina Campos Martín, Rosalía Rioja-Vázquez, Juan Antonio Irles Rocamora, Patricia Díaz Guardiola, Alejandro Sanz Paris, Pilar Matía Martín, Fátima Carabaña Pérez, Tomás Martín Folgueras, M ª Jesús Chinchetru, Luis Miguel Luengo Pérez, Cecilia Martínez Costa, Cristina Tejera Pérez, Carmen Arraiza Irigoyen, Olga Sánchez-Vilar Burdiel, Yaiza García Delgado, Miguel Á Ponce González, Sílvia Mauri Roca, María Victoria García Zafra, Marta Germán Díaz, Jesús M Morán López, Begoña Molina Baeza, Montserrat Gonzalo Marín, Rebeca Sánchez Sánchez, Alfonso Calañas Continente, Carmen Garde Orbaiz, Miguel Ángel Martínez Olmos, Clara Joaquín Ortiz, José Pablo Suárez Llanos, María de Talló Forga Visa, M ª Carmen Gil Martinez, María José Carrera Santaliestra, Susana Padín López, Gabriela Lobo, Antxón Apezetxea Celaya, Carmen Ballesta Sánchez, Anna Bonada Sanjaume, Bárbara Cánovas Gaillemin, Daniel Cardona Pera, Ignacio García Puente, Isabel Higuera Pulgar, Nuria Miserachs Aranda, María Dolores Del Olmo García, Samara Palma Milla, Rosa María Parés Marimón, Begoña Pintor de la Maza, Eva Ángeles Sánchez Martos
Aim: to communicate the home parenteral nutrition (HPN) data obtained from the HPN registry of the NADYA-SENPE group (www.nadya-senpe.com) for the year 2019. Material and methods: a descriptive analysis of the data collected from adult and pediatric patients with HPN in the NADYA-SENPE group registry from January 1 to December 31, 2019. Results: a total of 283 patients (51.9 % women), 31 children, and 252 adults from 47 Spanish hospitals were registered, which represents a prevalence rate of 6.01 patients per million inhabitants for year 2019...
December 9, 2021: Nutrición Hospitalaria: Organo Oficial de la Sociedad Española de Nutrición Parenteral y Enteral
#10
REVIEW
M Mutalib, J Kammermeier, R Vora, O Borrelli
Background: Intestinal pseudo obstruction both acute and chronic is an uncommon severe motility disorder that affect both children and adults, can lead to significant morbidity burden and have no standard management strategy. Prucalopride a highly selective serotonin receptor agonist is an effective laxative with reported extra colon action. We aim to report our experience in children with acute and chronic intestinal pseudo obstruction who responded to prucalopride and systemically review the use of prucalopride in intestinal pseudo obstruction...
July 2021: Acta Gastro-enterologica Belgica
#11
JOURNAL ARTICLE
Olivier Goulet, Anne Breton, Marie-Edith Coste, Béatrice Dubern, Emmanuelle Ecochard-Dugelay, Dominique Guimber, Irène Loras-Duclaux, Elie Abi Nader, Evelyne Marinier, Noel Peretti, Cecile Lambe
BACKGROUND AND AIMS: Home Parenteral Nutrition (HPN) is the cornerstone management for children suffering from chronic intestinal failure (CIF). In France, HPN is organized from a network of 7 certified centers located in University Hospitals spread across the national territory. This study aims to review the data involving children on HPN over a 6-years period in France to outline the global and continuous improvement in care. PATIENTS AND METHODS: This cross-sectional study included all children enrolled in any of the 7 French HPN certified centers from January 1st, 2014 to December 31st, 2019...
August 14, 2021: Clinical Nutrition
#12
JOURNAL ARTICLE
Dayoung Ko, Hee-Beom Yang, Joong Youn, Hyun-Young Kim
Chronic intestinal pseudo-obstruction (CIPO) is an extremely rare condition with symptoms of recurrent intestinal obstruction without any lesions. The outcomes of pediatric CIPO and predictors for the outcomes have not yet been well established. We analyzed the clinical outcomes and associated factors for the outcomes of pediatric CIPO. We retrospectively reviewed 66 primary CIPO patients diagnosed between January 1985 and December 2017. We evaluated parenteral nutrition (PN) factors such as PN duration, PN use over 6 months, home PN, and mortality as outcomes...
May 28, 2021: Journal of Clinical Medicine
#13
JOURNAL ARTICLE
Bismark Osei Sarfo, Hakan Kopdag, Marian-Christopher Pott, Lars Stiedenroth, Ulf Nahrstedt, Hansjörg Schäfer, Götz von Wichert
T-lymphocytic enteral leiomyositis (T-lel) is a rare disorder causing chronic intestinal pseudo-obstruction (CIPO), with cases predominantly being reported in the field of veterinary and pediatric medicine. Here, we present a case of T-lel-associated CIPO in an adult female, who initially presented with a paralytic ileus 2 weeks after a common gastroenteritis. The histological diagnosis was established through full-thickness bowel biopsy, exhibiting a dense lymphocytic infiltrate in the lamina muscularis of the intestinal wall...
April 2021: Zeitschrift Für Gastroenterologie
#14
JOURNAL ARTICLE
Elie Abi Nader, Cécile Lambe, Cécile Talbotec, Alexandre Acramel, Bénédicte Pigneur, Olivier Goulet
BACKGROUND & AIMS: Children on long-term home parenteral nutrition (HPN) are at increased risk of suboptimal growth and metabolic bone disease (MBD) i.e. decreased bone mineral density (BMD). The aims of this cross-sectional study were to assess growth and bone health in children on long term HPN and to identify risk factors for MBD. METHODS: Children above the age of 5 years, stable on HPN for more than 2 years were included. Medical files were reviewed retrospectively and included demographics, gestational age, birth weight and height, indication for PN, age at PN start, duration of PN, number of weekly PN infusions, weight-for-age and height-for-age (SD), body mass index (BMI, kg/m2 ) as well as blood and urine analyses at the time of Dual X-ray absorptiometry (DXA) measurements...
April 2021: Clinical Nutrition
#15
REVIEW
Letizia Zenzeri, Renato Tambucci, Paolo Quitadamo, Valentina Giorgio, Roberto De Giorgio, Giovanni Di Nardo
PURPOSE OF REVIEW: Chronic intestinal pseudo-obstruction (CIPO) is the most severe and disabling form of gastrointestinal dysmotility characterized by an impairment of coordinated propulsive activity in the gastrointestinal tract mimicking mechanical intestinal obstruction. Over the last few years, major advances have been made in the diagnostic and therapeutic management of this rare disorder. RECENT FINDINGS: The present narrative review aims to summarize the current literature about the management of CIPO focusing on significant novelties about definition, epidemiology, diagnosis, and therapeutic options...
May 2020: Current Opinion in Gastroenterology
#16
JOURNAL ARTICLE
Leonel Rodriguez, Nicole Heinz, Samuel Nurko
OBJECTIVES: Colon manometry (CM) has emerged as a tool to evaluate children with defecation problems. Our aim was to evaluate the utility of CM in guiding therapy and predicting surgery in pediatric constipation. METHODS: Retrospective review of children undergoing CM for 4 indications: constipation, fecal incontinence, postsurgical evaluation and chronic intestinal pseudo-obstruction. Variables included age, sex, follow-up, and CM parameters: gastrocolonic response (GC) and quality/quantity of high-amplitude propagating contractions (HAPCs)...
February 2020: Journal of Pediatric Gastroenterology and Nutrition
#17
JOURNAL ARTICLE
Suruchi Batra, Sheikh Rahman, Md Sohel Rana, Sravan Matta, Anil Darbari
BACKGROUND: Pediatric intestinal pseudo-obstruction is a rare disorder affecting gastrointestinal motility leading to chronic symptoms and hospitalizations. There is limited understanding of the epidemiology and healthcare burden. METHODS: We analyzed data from Kids' Inpatient Database from 2016, which includes inpatient discharge records from US hospitals. ICD-10 codes were used to identify patients 0-18 years with pediatric intestinal pseudo-obstruction and comorbid conditions...
April 2020: Neurogastroenterology and Motility: the Official Journal of the European Gastrointestinal Motility Society
#18
REVIEW
Heidi E Gamboa, Manu Sood
PURPOSE OF REVIEW: The purpose of this review is to discuss current knowledge on pediatric intestinal pseudo-obstruction. We will also review new mutations that have been identified through advancement in genetic testing, allowing for a better understanding of the underlying mechanisms of intestinal dysmotility and potential etiologies. RECENT FINDINGS: With the advancements in genetic testing, new mutations have been identified in the diagnosis of megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS), a disorder leading to pediatric pseudo-obstruction...
December 17, 2019: Current Gastroenterology Reports
#19
REVIEW
Loris Pironi, Anna Simona Sasdelli
Chronic intestinal pseudo-obstruction (CIPO) is a severe form of intestinal dysmotility disorder, characterized by the impairment of gastrointestinal propulsion of the gut content in the absence of fixed occluding lesions. CIPO is a rare disease that can develop in both children and adults. CIPO is classified as primary/idiopathic, when no underlying disorder is demonstrated, or secondary, when related to systemic diseases. Diagnosis relies on the finding of chronic/recurrent obstructive type symptoms with radiological features of dilated intestine with air/fluid levels without any lumen occluding lesion...
December 2019: Gastroenterology Clinics of North America
#20
JOURNAL ARTICLE
Leonel Rodriguez, Nicole Heinz, Samuel Nurko
Colon manometry (CM) has emerged as a tool to evaluate children with defecation problems. Our aim was to evaluate the utility of CM in guiding therapy and predicting surgery in pediatric constipation. METHODS: Retrospective review of children undergoing CM for 4 indications: constipation, fecal incontinence, post-surgical evaluation and chronic intestinal pseudo-obstruction. Variables included age, gender, follow up and CM parameters: gastrocolonic response (GC) and quality/quantity of high amplitude propagating contractions (HAPCs)...
September 17, 2019: Journal of Pediatric Gastroenterology and Nutrition
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