Takuma Arai, Ikuma Kato, Yusuke Kawabata, Shinichi Tsujimoto, Yoshihiro Ishikawa, Shingo Kato, Masanobu Takeyama, Shoji Yamanaka, Kenichi Kohashi, Yoshinao Oda, Satoshi Fujii
Myxoid pleomorphic liposarcoma (MPLS) is an extremely rare tumor listed in the fifth edition of the WHO classification (2020). Histologically, it mainly comprises a mixture of myxoid and pleomorphic liposarcoma-like components. Genetically, it lacks FUS/EWSR1::DDIT3 fusion and MDM2 amplification. Herein, we describe an example of MPLS with rhabdoid cells in a 10-year-old girl who presented with a growing mass in the right inguinal region. The specimen from the wide excision measured 68 mm × 55 mm × 43 mm, and a circumscribed and lobulated mass was observed in the subcutaneous tissue...
February 4, 2024: International Journal of Surgical Pathology