Generalized Congenital Epithelioid Blue Nevi (Pigmented Epithelioid Melanocytomas) in an Infant: Report of Case and Review of the Literature.

The epithelioid blue nevus (EBN) is a variant of the blue nevus characterized by heavily pigmented epithelioid melanocytes and lightly or nonpigmented spindle cells. It may be associated with Carney complex, a multiple neoplasia syndrome. Congenital cases of EBN not associated with Carney complex are rarely reported. We herein describe an infant who presented with multiple blue-gray nodules and papules involving the head, trunk, and extremities at birth, the corresponding histopathologic findings, and genetic testing results. This article is protected by copyright. All rights reserved.