Lymphaticovenular anastomosis for Klippel-Trenaunay-Weber syndrome.

INTRODUCTION: Since we performed lymphaticovenular anastomosis (LVA) for Klippel-Trenaunay-Weber syndrome and obtained relatively good results, we report the adaptation, effect of treatment, and mechanism of LVA.

PRESENTATION OF CASE: Case is a 28-year-old man with an increase of the circumference and pigment changes on the whole right leg and gluteal region from the time he was born. He exhibited signs of right leg cellulitis with a fever about 40° at frequency of the degree once a month. We planned to perform LVA of the right leg to prevent cellulitis of the lower limbs.

DISCUSSION: This case presented with repeated, severe cellulitis occurring once a month prior to treatment. This symptom greatly reduced the quality of life of the patient. Postoperatively, he lived his daily life with no particular limits, and significant improvement quality of life was due to LVA. Therefore, it is inferred that the protective efficacy of inflammation was obtained by anastomosing lymphatics and the vein around the skin lesions and a return current of the lymph flow was promoted.

CONCLUSION: The possibility that LVA could become an excellent therapy for similar cases is suggested.