Pigmented Melanotic Schwannoma of the Neck: Report of 2 Cases and Review of the Literature.

BACKGROUND:: Melanotic schwannoma is a rare tumor with indeterminate biologic behavior and varying treatment recommendations.

METHODS:: We report 2 cases of pigmented melanotic schwannoma of the head and neck and perform literature review. The pathologic and immunohistochemical characteristics of melanotic schwannoma are reviewed.

RESULTS:: Two cases of melanotic schwannoma are presented. Both cases underwent surgical resection with one patient receiving adjuvant radiation therapy.

CONCLUSIONS:: Melanotic schwannoma is a rare nerve sheath tumor that is frequently mistaken for malignant melanoma. We describe 2 cases of pigmented melanotic schwannoma of the head and neck with different presentations and review the histopathological and immunohistochemical features.