Klüver-Bucy syndrome after unilateral frontotemporal resection in a child with tuberous sclerosis

Susana Boronat, Peter Newberry, William Mehan, Elizabeth Anne Thiele, Ann-Christine Duhaime
Child's Nervous System: ChNS: Official Journal of the International Society for Pediatric Neurosurgery 2013, 29 (8): 1391-4
Klüver-Bucy syndrome (KBS) is a behavioral phenotype that appears most often after bilateral temporal damage. The main features of KBS are compulsion to examine objects orally, increased sexual activity, placidity, hypermetamorphosis (irresistible impulse to notice and react to everything within sight), visual agnosia, and problems with memory. It is more rarely reported in children than in adults. We present a case of KBS in a 2-year-old boy with tuberous sclerosis complex (TSC) after left frontotemporal resection for refractory epilepsy. This is the first KBS after unilateral temporal resection in a child, although it has already been reported in two adult cases. It also is the first case reported in a TSC patient.

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