JOURNAL ARTICLE

Treatment of apert syndrome: a long-term follow-up study

Karam A Allam, Derrick C Wan, Krit Khwanngern, Henry K Kawamoto, Neil Tanna, Adam Perry, James P Bradley
Plastic and Reconstructive Surgery 2011, 127 (4): 1601-11
21187805

BACKGROUND: Patients with Apert syndrome have severe malformations of the skull and face requiring multiple complex reconstructive procedures. The authors present a long-term follow-up study reporting both surgical results and psychosocial status of patients with Apert syndrome.

METHODS: A retrospective study was performed identifying patients with Apert syndrome treated between 1975 and 2009. All surgical procedures were recorded and a review of psychosocial and educational status was obtained when patients reached adulthood.

RESULTS: A total of 31 patients with Apert syndrome were identified; nine with long-term follow-up had complete records for evaluation. The average patient age was 30.4 years. Primary procedures performed included strip craniectomy and fronto-orbital advancement. Monobloc osteotomy and facial bipartition were performed in eight patients, and all underwent surgical orthognathic correction. Multiple auxiliary procedures were also performed to achieve better facial symmetry. Mean follow-up after frontofacial advancement was 22.5 years. Psychosocial evaluation demonstrated good integration of patients into mainstream life.

CONCLUSIONS: This report presents one of the longest available follow-up studies for surgical correction of patients with Apert syndrome. Although multiple reconstructive procedures were necessary, they play an important role in enhancing the psychosocial condition of the patients, helping them integrate into mainstream life.

Full Text Links

Find Full Text Links for this Article

Discussion

You are not logged in. Sign Up or Log In to join the discussion.

Related Papers

Remove bar
Read by QxMD icon Read
21187805
×

Save your favorite articles in one place with a free QxMD account.

×

Search Tips

Use Boolean operators: AND/OR

diabetic AND foot
diabetes OR diabetic

Exclude a word using the 'minus' sign

Virchow -triad

Use Parentheses

water AND (cup OR glass)

Add an asterisk (*) at end of a word to include word stems

Neuro* will search for Neurology, Neuroscientist, Neurological, and so on

Use quotes to search for an exact phrase

"primary prevention of cancer"
(heart or cardiac or cardio*) AND arrest -"American Heart Association"

We want to hear from doctors like you!

Take a second to answer a survey question.