keyword
https://read.qxmd.com/read/36634578/-congenital-heart-disease-in-down-s-syndrome
#21
JOURNAL ARTICLE
Rebeca Arias-Lobo, Edgar Lupinta-Paredes, Juan Calderón-Colmenero, Jorge L Cervantes-Salazar, José A García-Montes, Emilia J Patiño-Bahena, Antonio Benita-Bordes
BACKGROUND: Down syndrome is the most common chromosomal abnormality, it is associated with a wide variety of congenital heart defects, being considered as clinical elements of high infant morbidity and mortality. Objective. OBJECTIVE: To describe the clinical outcomes of patients with Down syndrome undergoing surgery and interventionism as treatment for congenital heart disease at this Institution. MATERIAL AND METHODS: 368 patients with Down syndrome and associated congenital heart disease were diagnosed...
January 12, 2023: Archivos de Cardiología de México
https://read.qxmd.com/read/36425912/anaesthetic-management-of-a-child-with-unrepaired-complete-atrioventricular-canal-defect-double-outlet-ventricle-and-pulmonary-stenosis-for-non-cardiac-surgery
#22
JOURNAL ARTICLE
Sukhyanti Kerai, Prachi Gaba, Lalit Gupta, Kirti N Saxena
No abstract text is available yet for this article.
October 2022: Indian Journal of Anaesthesia
https://read.qxmd.com/read/36203987/spinal-dural-arteriovenous-fistula-a-rare-but-treatable-disease-that-should-not-be-missed-by-orthopedic-surgeons
#23
JOURNAL ARTICLE
Baohui Yang, Teng Lu, Xijing He, Haopeng Li
Objective: Spinal dural arteriovenous fistula (SDAVF) is a rare disease that is often misdiagnosed by orthopedic surgeons. We analyzed the reasons for the misdiagnosis and proposed countermeasures. Methods: Twenty-two SDAVF patients who were initially treated in orthopedics were included. The patients were divided into a correct diagnosis group (A) and a misdiagnosis group (B). The clinical data and prognosis were evaluated. Results: There were 10 patients in group A and 12 patients in group B...
2022: Frontiers in Neurology
https://read.qxmd.com/read/36168722/predictors-of-increased-postoperative-length-of-stay-after-complete-atrioventricular-canal-repair
#24
JOURNAL ARTICLE
Alyssa C Habermann, James M Meza, Ashley N Dischinger, Lillian Kang, Neel K Prabhu, Abigail R Benkert, Joseph W Turek, Nicholas D Andersen
BACKGROUND: The optimal timing of surgical repair for infants with complete atrioventricular canal defect remains controversial, as there are risks to both early and late repair. We address this debate by investigating the association of various risk factors, including age and weight at surgery, markers of failure to thrive, and pulmonary vascular disease, with postoperative length of stay following complete atrioventricular canal repair. METHODS: Infants who underwent repair of complete atrioventricular canal were identified from our institutional Society of Thoracic Surgeons Congenital Heart Surgery Database...
September 28, 2022: Cardiology in the Young
https://read.qxmd.com/read/36126337/rare-association-of-absent-pulmonary-valve-syndrome-complete-atrioventricular-canal-defect-double-outlet-right-ventricle-right-aortic-arch-and-aberrant-right-subclavian-artery-in-a-fetal-case
#25
Eviç Zeynep Başar, Yasemin Doğan, Ahmet Şaşmazel, Kadir Babaoğlu
Absent pulmonary valve syndrome (APVS) is a rare congenital cardiac anomaly. It is often associated with TOF, but may also be associated with an intact ventricular septum or, more rarely, with tricuspid atresia. It's combination with a complete atrioventricular septal defects and double outlet right ventricle has been reported extremely rare, even in the postnatal period. Herein, we report a 20-week-old fetus with a right aortic arch and an aberrant left subclavian artery with this rare combination. We report a case of a 20-week fetus diagnosed having this rare combination of right aortic arch and aberrant left subclavian artery...
September 20, 2022: Echocardiography
https://read.qxmd.com/read/36045487/myocardial-development-in-crocodylians
#26
JOURNAL ARTICLE
Alena Kvasilova, Martina Gregorovicova, Veronika Olejnickova, Hana Kolesova, David Sedmera
BACKGROUND: Recent reports confirmed the notion that there exists a rudimentary cardiac conduction system (CCS) in the crocodylian heart, and development of its ventricular part is linked to septation. We thus analyzed myocardial development with the emphasis on the CCS components and vascularization in two different crocodylian species. RESULTS: Using optical mapping and HNK-1 immunostaining pacemaker activity was localized to the right-sided sinus venosus. The atrioventricular conduction was restricted to dorsal part of the atrioventricular canal...
August 31, 2022: Developmental Dynamics
https://read.qxmd.com/read/35979598/surgical-repair-of-complete-common-atrioventricular-canal-in-a-conjoined-twin-following-separation
#27
JOURNAL ARTICLE
Stephen H Fatuzzo, Jason W Greenberg, Russel Hirsch, Ilias D Iliopoulos, Michael D Taylor, David L S Morales
Congenital heart disease (CHD) is common in conjoined twins but reports of surgical repair in this population are rare. We present the case of a conjoined twin diagnosed prenatally with a complete common atrioventricular canal defect (CAVC). Due to wound complications from twin separation, definitive repair was deferred and pulmonary arterial banding was performed initially. At 6 months, a complete CAVC repair was performed. The present case adds to the literature on successful cardiac surgical repairs in conjoined twins...
August 17, 2022: World Journal for Pediatric & Congenital Heart Surgery
https://read.qxmd.com/read/35678827/conduction-system-pacing-in-pediatrics-and-congenital-heart-disease-a-single-center-series-of-24-patients
#28
JOURNAL ARTICLE
Amanda Gordon, Erick Jimenez, Daniel Cortez
His-bundle pacing has demonstrated feasibility in numerous adult studies to reverse and prevent pacing-induced cardiomyopathy, however, is met with higher capture thresholds with deployment sheaths designed for adults with his-bundles in the typical location. To describe 24 pediatric and adult congenital patients post-physiologic pacing. Patients at the University of Minnesota Masonic Children's Hospital with congenital complete heart block or congenital heart disease and atrioventricular block presented for pacemaker placement between November 2019 and January 2021...
June 9, 2022: Pediatric Cardiology
https://read.qxmd.com/read/35621846/a-rare-case-of-polysplenia-syndrome-associated-with-severe-cardiac-malformations-and-congenital-alveolar-dysplasia-in-a-one-month-old-infant-a-complete-macroscopic-and-histopathologic-study
#29
Cosmin Ioan Mohor, Sorin Radu Fleaca, Alexandra Oprinca Muja, George Calin Oprinca, Mihai Dan Roman, Radu Chicea, Adrian Gheorghe Boicean, Horatiu Dura, Ciprian Tanasescu, Nicolas Catalin Ionut Ion, Mihai Faur, Ciprian Ionut Bacila, Florina Batar, Calin Ilie Mohor
Polysplenia syndrome represents a type of left atrial isomerism characterized by multiple small spleens, often associated with cardiac malformations and with situs ambiguus of the abdominal organs. The case presented is of a one-month-old male infant, weighing approximately 3000 g, born at the County Clinical Emergency Hospital of Sibiu, who was hospitalized from birth until death. The patient suffered cardio-respiratory arrest due to severe hypoxia and septicemia on the background of a series of complex cardiac malformations associated with congenital abdominal organ anomalies...
April 27, 2022: Journal of Cardiovascular Development and Disease
https://read.qxmd.com/read/35597538/surgical-obliteration-of-a-posterior-fossa-dural-arteriovenous-fistula-presenting-with-exclusive-spinal-signs-and-symptoms-caused-by-spinal-cord-venous-hypertension
#30
MirHojjat Khorasanizadeh, Max Shutran, Christopher S Ogilvy
Vascular malformations in the dura of the spinal root sleeve in the thoracic or lumbar region can cause venous hypertension with resultant spinal cord edema and neurologic deterioration. However, occasionally an intracranial vascular malformation can have venous drainage into the spinal canal causing symptoms, signs, and radiographic appearance that can mimic spinal lesions. Herein, we present the case of a 73-year-old man who developed lower extremity weakness and loss of sensation. The patient initially underwent L4-L5 diskectomy elsewhere, but the symptoms progressed...
May 18, 2022: World Neurosurgery
https://read.qxmd.com/read/35537615/visualization-and-quantification-of-the-unrepaired-complete-atrioventricular-canal-valve-using-open-source-software
#31
JOURNAL ARTICLE
Hannah H Nam, Christian Herz, Andras Lasso, Alana Cianciulli, Maura Flynn, Jing Huang, Zi Wang, Beatriz Paniagua, Jared Vicory, Saleha Kabir, John Simpson, David Harrild, Gerald Marx, Meryl S Cohen, Andrew C Glatz, Matthew A Jolley
BACKGROUND: Repair of complete atrioventricular canal (CAVC) is often complicated by residual left atrioventricular valve regurgitation. The structure of the mitral and tricuspid valves in biventricular hearts has previously been shown to be associated with valve dysfunction. However, the three-dimensional (3D) structure of the entire unrepaired CAVC valve has not been quantified. Understanding the 3D structure of the CAVC may inform optimized repair. METHODS: Novel open-source work flows were created in SlicerHeart for the modeling and quantification of CAVC valves on the basis of 3D echocardiographic images...
September 2022: Journal of the American Society of Echocardiography
https://read.qxmd.com/read/35460862/canadian-cardiovascular-society-2022-guidelines-for-cardiovascular-interventions-in-adults-with-congenital-heart-disease
#32
Ariane Marelli, Luc Beauchesne, Jack Colman, Robin Ducas, Jasmine Grewal, Michelle Keir, Paul Khairy, Erwin Oechslin, Judith Therrien, Isabelle F Vonder Muhll, Rachel M Wald, Candice Silversides, David J Barron, Lee Benson, Pierre-Luc Bernier, Eric Horlick, Réda Ibrahim, Giuseppe Martucci, Krishnakumar Nair, Nancy C Poirier, Heather J Ross, Helmut Baumgartner, Curt J Daniels, Michelle Gurvitz, Jolien W Roos-Hesselink, Adrienne H Kovacs, Christopher J McLeod, Barbara J Mulder, Carole A Warnes, Gary D Webb
Interventions in adults with congenital heart disease (ACHD) focus on surgical and percutaneous interventions in light of rapidly evolving ACHD clinical practice. To bring rigour to our process and amplify the cumulative nature of evidence ACHD care we used the ADAPTE process; we systematically adjudicated, updated, and adapted existing guidelines by Canadian, American, and European cardiac societies from 2010 to 2020. We applied this to interventions related to right and left ventricular outflow obstruction, tetralogy of Fallot, coarctation, aortopathy associated with bicuspid aortic valve, atrioventricular canal defects, Ebstein anomaly, complete and congenitally corrected transposition, and patients with the Fontan operation...
July 2022: Canadian Journal of Cardiology
https://read.qxmd.com/read/35403044/intraoperative-conduction-mapping-in-complex-congenital-heart-surgery
#33
JOURNAL ARTICLE
Eric N Feins, Edward T O'Leary, David M Hoganson, Noah Schulz, Emily Eickoff, Jocelyn Davee, John K Triedman, Christopher W Baird, Pedro J Del Nido, Sitaram Emani, Elizabeth S DeWitt
Objective: Postoperative heart block is a significant problem in congenital heart surgery because of the unpredictability and variability of conduction tissue location in complex congenital heart defects. A novel technique for intraoperative conduction system mapping during complex congenital heart surgery is described. Methods: Intraoperative conduction system mapping was performed utilizing a high-density multielectrode grid catheter to collect intracardiac electrograms on open, beating hearts during repair of complex congenital heart defects...
April 2022: JTCVS techniques
https://read.qxmd.com/read/35364233/transcatheter-leadless-permanent-pacemaker-in-complex-congenital-heart-disease-with-interrupted-inferior-vena-cava-a-challenging-implantation
#34
Babu Ezhumalai, Jitendra Singh Makkar
31 years lady with complete atrioventricular canal defect, large primum atrial septal defect (ASD), inlet ventricular septal defect (VSD) and Eisenmenger syndrome, presented with atrial flutter and complete heart block. She was not suitable for corrective cardiac surgery and not yet indicated for heart-lung transplantation. She was advised single chamber permanent pacemaker and eventually Micra transcatheter leadless pacemaker was finalised for her. Transcatheter leadless pacemaker was deployed in her RV septum despite some unforeseen technical problems...
March 29, 2022: Indian Pacing and Electrophysiology Journal
https://read.qxmd.com/read/34940530/common-arterial-trunk-associated-with-functionally-univentricular-heart-anatomical-study-and-review-of-the-literature
#35
JOURNAL ARTICLE
Sami Chatila, Lucile Houyel, Manon Hily, Damien Bonnet
Common arterial trunk (CAT) is a rare congenital heart disease that is commonly included into the spectrum of conotruncal heart defects. CAT is rarely associated with functionally univentricular hearts, and only few cases have been described so far. Here, we describe the anatomical characteristics of CAT associated with a univentricular heart diagnosed in children and fetuses referred to our institution, and we completed the anatomical description of this rare condition through an extensive review of the literature...
December 6, 2021: Journal of Cardiovascular Development and Disease
https://read.qxmd.com/read/34828742/antenatal-diagnosis-of-a-partial-atrioventricular-canal-with-ebstein-s-anomaly
#36
Gerald Laforest, Jean-Bernard Selly, Gilbert Dubois, Bernard Kreitmann, Yael Levy
The simultaneous occurrence of an atrioventricular canal defect (AVCD) and Ebstein's anomaly is extremely rare, occurring in less than 0.5% of all patients with AVCD. Only 22 cases are described in the literature. This patient's antenatal diagnosis of both Ebstein's anomaly and partial AVCD was made at 25 weeks of gestation. The delivery was organized in a tertiary center. The initial neonatal course was difficult but with adequate treatment, a rapid improvement allowed for a gap of almost 2 years before a complete surgical repair including a cone tricuspid plasty...
November 10, 2021: Children
https://read.qxmd.com/read/34729452/covid-19-congenital-heart-disease-and-pregnancy-dramatic-conjunction-case-report
#37
Walkiria Samuel Avila, Marcelo Kirschbaum, Marcela Santana Devido, Lea Maria Macruz Ferreira Demarchi
BACKGROUND: Epidemiological data from the COVID-19 pandemic report that patients with pre-existing cardiovascular disease have worse outcomes and higher mortality, and that pregnant women should be considered at high risk. CASE SUMMARY: A 25-year-old pregnant woman on the waiting list for a heart transplant, with a history of complete atrioventricular canal surgery, mitral mechanical prosthetic implant (St Jude-27), and cardiac resynchronization therapy (Boston Scientific) was hospitalized at 30 weeks of gestation for treatment of heart failure...
October 2021: European Heart Journal. Case Reports
https://read.qxmd.com/read/34696553/transvenous-coil-embolization-of-hypoglossal-canal-dural-arteriovenous-fistula-using-detachable-coils-a-case-report
#38
Su Min Kye, Jun Hyong Ahn, Heui Seung Lee, Ji Hee Kim, Jae Keun Oh, Joon Ho Song, In Bok Chang
The hypoglossal canal (HC) is an unusual location of the posterior fossa dural arteriovenous fistula (AVF), which usually occurs in the transverse or sigmoid sinus. Herein, we report a case of HC dural AVF successfully treated with transvenous coil embolization using detachable coils in a 68-year-old woman who presented with headache and left pulsatile tinnitus for 2 months. Brain magnetic resonance imaging (MRI) and cerebral angiography revealed left HC dural AVF. The pulsatile bruit disappeared immediately after the procedure...
June 2022: Journal of Cerebrovascular and Endovascular Neurosurgery
https://read.qxmd.com/read/34662933/direct-superior-ophthalmic-vein-approach-to-treat-anterior-condylar-confluence-dural-arteriovenous-fistula
#39
JOURNAL ARTICLE
Rasmiranjan Padhi, Sathish Kandasamy, Balasenthil Kumaran, Naci Kocer, Harshith Karmadhari
Dural arteriovenous fistulas (DAVFs) are acquired pathological arteriovenous connections involving vessels that usually supply the meninges. A DAVF in the region of the hypoglossal canal is a rare form of fistula that involves the anterior condylar confluence or anterior condylar vein. We report a case of hypoglossal canal DAVF that was successfully embolized transvenously through a superior ophthalmic vein (SOV) approach. After failed attempts through jugular access, our patient was treated by a unique percutaneous direct puncture approach through the SOV, achieving complete obliteration of the fistula...
November 2021: Neurointervention
https://read.qxmd.com/read/34633029/correlation-of-ventricular-septal-defect-height-and-outcomes-after-complete-atrioventricular-septal-defect-repair
#40
JOURNAL ARTICLE
Laura S Fong, David Youssef, Julian Ayer, Ian A Nicholson, David S Winlaw, Yishay Orr
OBJECTIVES: There are limited data available on the height of the ventricular component of the septal deficiency (VSD) in patients undergoing complete atrioventricular septal defect (CAVSD) repair. VSD height may influence optimal choice of repair strategy with potential consequences for long-term outcomes. We aimed to measure VSD height using 2-dimensional echocardiography and review its association with postoperative outcomes. METHODS: We retrospectively reviewed the preoperative echocardiograms of 45 consecutive patients who underwent CAVSD repair between May 2010 and December 2015 at a single centre...
February 21, 2022: Interactive Cardiovascular and Thoracic Surgery
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