Domenico Corrado, Aris Anastasakis, Cristina Basso, Barbara Bauce, Carina Blomström-Lundqvist, Chiara Bucciarelli-Ducci, Alberto Cipriani, Carlo De Asmundis, Estelle Gandjbakhch, Juan Jiménez-Jáimez, Maria Kharlap, William J McKenna, Lorenzo Monserrat, James Moon, Antonis Pantazis, Antonio Pelliccia, Martina Perazzolo Marra, Kalliopi Pillichou, Jeanette Schulz-Menger, Ruxandra Jurcut, Petar Seferovic, Sanjay Sharma, Jacob Tfelt-Hansen, Gaetano Thiene, Thomas Wichter, Arthur Wilde, Alessandro Zorzi
Arrhythmogenic cardiomyopathy (ACM) is a heart muscle disease characterized by prominent "non-ischemic" myocardial scarring predisposing to ventricular electrical instability. Diagnostic criteria for the original phenotype, arrhythmogenic right ventricular cardiomyopathy (ARVC), were first proposed in 1994 and revised in 2010 by an international Task Force (TF). A 2019 International Expert report appraised these previous criteria, finding good accuracy for diagnosis of ARVC but a lack of sensitivity for identification of the expanding phenotypic disease spectrum, which includes left-sided variants, i...
January 15, 2024: International Journal of Cardiology