Syed Wajahat Ali Rizvi, Syed Ali Raza Rizvi, Shagufta Qadri, Saifullah Khalid, Mohammed Azfar Siddiqui, Adeeb Alam Khan, Afeefa Akhter
Malignant peripheral nerve sheath tumor of the orbit is an exceedingly rare entity. These tumors exhibit locally aggressive behavior, recurrences, distant metastasis, and poor response to existing treatment protocols. Orbital nerve sheath tumors are often associated with neurofibromatosis 1, and malignant transformation of neurofibroma into malignant nerve sheath tumor has also been seen. The recommended treatment for localized disease is radical or wide surgical excision to achieve negative margins followed by chemoradiation...
2024: Oman Journal of Ophthalmology