Bresciani Lorenzo, Salvalaggio Alessandro, Vegezzi Elisa, Visentin Andrea, Fortuna Andrea, Anglani Mariagiulia, Cacciavillani Mario, Stefano Masciocchi, Silvia Scaranzin, Carecchio Miryam, Martinuzzi Andrea, Gastaldi Matteo, Briani Chiara
AIM: Nodo- and paranodopathies are autoimmune neuropathies associated with antibodies to nodal-paranodal antigens (neurofascin 140/186 and 155, contactin-1, contactin-associated protein 1 [Caspr1] characterized by peculiar clinical features, poor response to standard immunotherapies (e.g, intravenous immunoglobulins, IVIg). Improvement after anti-CD20 monoclonal antibody therapy has been reported. Data on Caspr1 antibodies pathogenicity are still preliminary, and longitudinal titers have been poorly described...
May 29, 2023: Journal of the Peripheral Nervous System: JPNS