Sara Moutinho-Pereira, Francisca Beires, Joana Dos Santos, Maria Relvas, Leonor Castendo Ramos, Sara Castendo Ramos, Teresa Medeiros, Helena Greenfield, Sara Augusta Ramos, Pedro Andrade
Febrile ulceronecrotic Mucha-Habermann disease is a rare and severe variant of pityriasis lichenoides, characterized by sudden onset of generalized ulceronecrotic papules that rapidly coalesce into ulcers associated with high fever. Systemic manifestations such as intravascular disseminated coagulation and pulmonary, cardiac, gastrointestinal, and central nervous system involvement are common. Treatment is based on oral corticosteroids, immunosuppressive drugs such as methotrexate, and general supportive treatment...
April 15, 2024: Dermatology Online Journal